Anesthetic management of a glycogen storage disease type 1a with air embolism during liver transplantation: a case report

HIGHLIGHTS

• who: Emre Kandemir* from the Department of, Bau015fkent University Faculty of Medicine, Ankara, Turkey have published the paper: Anesthetic Management of a Glycogen Storage Disease Type 1a with Air Embolism During Liver Transplantation: A Case Report, in the Journal: (JOURNAL)

SUMMARY

Glycogen storage disease type 1a (GSD-1a) is a rare autosomal recessive inborn error of metabolism caused by deficient activity of glucose-6-phosphatase (G6Pase). Clinically, patients present with severe fasting intolerance, failure to thrive, and hepatomegaly. Orthotopic liver transplantation (OLT) may be considered in patients with difficult metabolic control and hepatic . . .

 



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